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Cogan syndrome
Cogan syndrome is a rare autoimmune systemic vasculitis characterized by intraocular inflammation and vestibuloauditory dysfunction
Prevalence
1.5-2.5 / 100,000
N/A
US Estimated
N/A
Europe Estimated
Age of Onset
ICD-10
H16.3
Inheritance
This condition does not appear to have a clear pattern of inheritance.
Rare View
Cogan Syndrome is a rare autoimmune disorder primarily characterized by inflammation of the eyes and inner ears, leading to vision and hearing impairments. The exact cause remains unclear, but it is believed to involve an autoimmune response where the body's immune system mistakenly attacks its own tissues.
5 Facts you should know
FACT
Cogan syndrome (CS) is a chronic inflammatory disorder that most commonly affects young adults
FACT
Clinical hallmarks are interstitial keratitis (IK) and vestibuloauditory dysfunction
FACT
There is no known gender or racial predominance
FACT
The predominant ocular feature of CS is interstitial keratitis (IK), which typically causes eye redness, pain, photophobia, and blurred vision
FACT
The inner ear manifestations of CS are episodes of vertigo, ataxia, nausea, vomiting, tinnitus, and hearing loss